Case Report

Pachyonychia Congenita: A Case Report


  • Mohammad Abid Keen
  • Iffat Hassan

J Turk Acad Dermatol 2014;8(2):0-0


Pachyonychia congenita is an autosomal dominant genodermatosis characterized by subungual hyperkeratosis of the distal n ails and focal palmoplantar hyperkeratosis. It is classified as pachyonychia congenita type 1 (Jadassoh n-Lewandowsky) and pa chyonychia cong enita type 2 (J ackson- Lawler) s yndrome s. Herein a case of Pachyo nych ia conge nita type 1 i n a m iddle ag ed Kashmiri female is reported in view of the clinical rarity of this condition.

Keywords: Pachyonychia congenita, autosomal dominant, subungual hyperkeratosis, palmoplantar hyperkeratosis