Case Report

Familial En Coupe De Sabre In Two Indian Siblings with Becker’s Nevus: A Unique Rare Presentation


  • Vibhu Mendiratta
  • Nikita Gandhi
  • Soumya Agarwal
  • Ram Chander

J Turk Acad Dermatol 2016;10(2):0-0


En coup de sabre (frontoparietal morphea), also known as localized scleroderma, is characterized by thickening or hardening of the skin and subcutaneous tissue as a result of excess collagen deposition. Familial morphea is uncommon with only around 20 cases reported to date. To the best of our knowledge, our case reports are the only other reported case of familial en coup de sabre and the second case of horizontal transmission. There is only a single case report of coexistence of morphea and Becker’s nevus so far. This report adds a unique case of concomitance of Becker’s melanosis with familial en coupe de sabre to the medical literature.

Keywords: Collagen vascular diseases, connective tissue diseases